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A Late Onset of Adrenocortical Cancer Assosiated with Beckwith-Wiedemann Syndrome

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Abstract


Beckwith-Wiedemann syndrome (BWS) is a genetic overgrowth disorder involving a predisposition to tumor development. The common features of Beckwith-Wiedemann syndrome include omphalocele, macroglos- sia and macrosomia. The increased risk for neoplasia is concentrated in the first eight years of life. However, this case presents a late onset of adrenocortical cancer assosiated with Beckwith-Wiedemann syndrome.

N S Kuznetsov

Endocrinology Research Centre

N V Latkina

Endocrinology Research Centre

N Yu Kalinchenko

Endocrinology Research Centre

L S Selivanova

Endocrinology Research Centre

A O Raykhman

Email: toda_mi_alma@inbox.ru
I.M. Sechenov First Moscow State Medical University

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